NEET PG Medical – 2019 – Question – 32
Zewellger syndrone is due to absence of
a) Lysosomal
b) Mitochondria
c) Peroxisome
d) Nucleus
Show Answer
Correct Answer – C
Answer. C. Peroxisome
- Zellweger syndrome, also called cerebrohepatorenal syndrome, is a rare congenital disorder characterized by the reduction or absence of functional peroxisomes in the cells of an individual.
- Zellweger syndrome is associated with impaired neuronal migration, neuronal positioning, and brain development.
- In addition, individuals with Zellweger syndrome can show a reduction in central nervous system (CNS) myelin (particularly cerebral), which is referred to as hypomyelination.