NEET PG Medical – 2018 – Question – 37
Bernard–Soulier syndrome due to deficiency of
a) Gp 2b/3a
b) Gp 1b
c) vWf
d) TNF
Show Answer
Correct Answer – B
Answer: B. Gp 1b
Bernard–Soulier syndrome (BSS) / Hemorrhagic Parous Thrombocytic Dystrophy
Rare autosomal recessive coagulopathy
Causes a deficiency of glycoprotein 1b (Gp1b), receptor for von Willebrand factor.